Official Title
A Phase 2/3, Randomized, Open-label, Parallel Group, 3-arm, Multicenter Study Investigating the Efficacy and Safety of Intravenous Administrations of Emapalumab, an Anti-interferon Gamma (Anti-IFNγ) Monoclonal Antibody, and Anakinra, an Interleukin-1(IL-1) Receptor Antagonist, Versus Standard of Care, in Reducing Hyper-inflammation and Respiratory Distress in Patients With SARS-CoV-2 Infection.
Brief Summary

Hyper-inflammation, caused by a cytokine storm resulting from an exaggerated response of the immune system in the presence of severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2), is considered to represent one of the most important negative prognostic factors in patients infected with sSARS-CoV-2. The objective of this study is to investigate new treatment options to reduce the number of patients requiring mechanical ventilation. This is intended to address the most urgent need to preserve the access to intensive care unit support to the lowest possible number of patients and may potentially reduce mortality.

Detailed Description

This is an open label, controlled, parallel group, 3-arm, multicenter study to assess the
efficacy and safety of Emapalumab or Anakinra, versus standard of care (SoC). Patients
between 30 and 80 years will be eligible to participate in the study. The study is planned to
consist of three groups, each comprising 18 patients. Treatment will be randomized to either
Emapalumab+SoC, Anakinra+SoC or only SoC for two weeks. Follow-up visit or phone calls will
be made 4 and 8 weeks after end of treatment period.

Terminated
SARS-CoV-2

Biological: Emapalumab

I.v. infusion every third day
Other Name: Gamifant

Biological: Anakinra

Daily i.v. infusion
Other Name: Kineret

Eligibility Criteria

Inclusion Criteria:

1. Signed informed consent provided by the patient, or by the patient's legally
authorized representative(s), as applicable.

2. Documented presence of SARS-CoV-2 infection as per hospital routine.

3. Age > 18 to < 85 years at the time of screening.

4. Presence of respiratory distress, defined as:

1. PaO2/FiO2 < 300 mm Hg and >200 mm Hg or

2. Respiratory Rate (RR) ≥30 breaths/min or

3. SpO2 < 93 percent in air at rest. Note: Patients given continous positive airway
pressure (CPAP) ventilator support are eligible for inclusion.

Presence of hyperinflammation defined as:

1. Lymphocyte counts:

- < 1000 cells/µL, in patients who have not received systemic glucocorticoids for
at least 2 days prior to the assessment of the lymphocyte count

- < 1200 cells/µL, in patients who have received systemic glucocorticoids for at
least 2 days prior to the assessment of the lymphocyte count

and

2. One of the following three criteria:

i. Ferritin > 500ng/mL

ii. LDH > 300 U/L

iii. D-Dimers > 1000 ng/mL

Exclusion Criteria:

1. Patients in mechanical ventilation or with modified early warning score (MEWS) >4 with
evidence of moderate or above ARDS (Berlin definition, namely with PaO2/FiO2 >100, but
<200 mm Hg) or severe respiratory insufficiency or evidence of rapid worsening
(respiratory distress requiring mechanical ventilation or presence of shock or
presence of concomitant organ failure requiring ICU admission). Note: For the
evaluation of patient eligibility, temperature will not be considered in the
calculation of the total MEWS score since presence of fever is a hallmark of
SARS-CoV-2 infection

2. Impairment of cardiac function defined as poorly controlled heart diseases, such as
New York heart association (NYHA) class II (mild) and above, cardiac insufficiency,
unstable angina pectoris, myocardial infarction within 1 year before enrollment,
supraventricular or ventricular arrhythmia need treatment or intervention.

3. Severe renal dysfunction (estimated glomerular filtration rate ≤ 30 mL/min/1.73 m2) or
receive continuous renal replacement therapy, hemodialysis, or peritoneal dialysis.

4. Uncontrolled hypertension (seated systolic blood pressure >180 mmHg, or diastolic
blood pressure >110mmHg) .

5. Administration of plasma from convalescent patients who recovered from SARS-CoV-2
infection.

6. Clinical suspicion of latent tuberculosis.

7. History of hypersensitivity or allergy to any component of the study drug.

8. Pregnant women.

9. Existence of any life-threatening co-morbidity or any other medical condition which,
in the opinion of the investigator, makes the patient unsuitable for inclusion.

10. Enrollment in another concurrent clinical interventional study, or intake of an
investigational drug within three months or 5 half-lives prior to inclusion in this
study, if considered interfering with this study objectives as assessed by the
Investigator.

11. Foreseeable inability to cooperate with given instructions or study procedures.

12. Clinical suspicion of active mycobacteria, histoplasma capsulatum, herpes zoster,
salmonella, and shigella Infections.

13. Patients with liver dysfunction defined as AST or ALT > 5 × ULN

Eligibility Gender
All
Eligibility Age
Minimum: 18 Years ~ Maximum: 85 Years
Countries
Italy
United States
Locations

Regions hospital
Saint Paul, Minnesota, United States

The Valley hospital
Ridgewood, New Jersey, United States

NewYork-Presbyterian Queens
Flushing, New York, United States

Temple University Hospital
Philadelphia, Pennsylvania, United States

University of Utah Health
Salt Lake City, Utah, United States

ASST Spedali Civili di Brescia Dipartimento di Reumatologia e Immunologia Clinica
Brescia, Italy

S.C. Malattie Infettive, Ospedale Galliera
Genova, Italy

Ospedale Maggiore Policlinico, Dipartimento di Anestesia-Rianimazione e Medicina di Urgenza
Milano, Italy

Dipartimento di Medicina - DIMED, Azienda Ospedale - Università Padova
Padova, Italy

Azienda Ospedaliero-Universitaria di Parma, Dipartimento di Malattie infettive ed epatologia
Parma, Italy

Ospedale Lazzaro Spallanzani, Dipartimento di Malattie Infettive ad alta Intensità di cura ed altamente contagiose,Ospedale Lazzaro Spallanzani
Roma, Italy

ASL Città di Torino, Unit of Infectious Diseases, Medicine, Rheumatology
Torino, Italy

Emanuele Nicastri, MD, Principal Investigator
Direttore Dipartimento di Malattie Infettive

Swedish Orphan Biovitrum
NCT Number
MeSH Terms
Infections
Interleukin 1 Receptor Antagonist Protein